Hypertrophic pyloric stenosis.pptx
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Hypertrophic pyloric stenosis is a condition in infants where the pyloric muscle thickens, causing projectile vomiting. It is usually diagnosed between 4-8 weeks of age when vomiting becomes frequent and forceful. On physical exam, doctors may feel an olive-sized pyloric tumor. Ultrasound confirms the diagnosis by showing thickened pyloric muscles. The standard treatment is Ramstedt pyloromyotomy surgery to cut the thickened pyloric muscle. After resuscitation from dehydration, the surgery cures the condition and babies can resume feedings within a day.
Hypertrophic pyloric stenosis.pptx
- 1. Hypertrophic pyloric stenosis Dr. RUTAYISIRE François Xavier PGY1 Common surgical conditions module University of Rwanda Lecturer: Prof. Ntaganda Edmond
- 2. Hypertrophic pyloric stenosis (HPS) • HPS causes a functional gastric outlet obstruction as a result of hypertrophy and hyperplasia of the muscular layers of the pylorus. • In infants, HPS is the most common cause of gastric outlet obstruction and the most common surgical cause of vomiting. • Hirschsprung wrote the first complete description of hypertrophic pyloric stenosis (HPS) in 1888. • In 1907, Ramstedt described an operation to alleviate this condition. He suggested splitting the pyloric muscle and leaving it open to heal secondarily. • This procedure has been used to treat hypertrophic pyloric stenosis (HPS) since that time.
- 3. Signs and symptoms • Typical presentation is onset of initially nonbloody, usually nonbilious vomiting at 4-8 weeks of age • Although vomiting may initially be infrequent, over several days it becomes more predictable, occurring at nearly every feeding • Vomiting intensity also increases until pathognomonic projectile vomiting ensues • Slight hematemesis of either bright-red flecks or a coffee-ground appearance is sometimes observed • Patients are usually not ill-looking or febrile; the baby in the early stage of the disease remains hungry and sucks vigorously after episodes of vomiting • Prolonged delay in diagnosis can lead to dehydration, poor weight gain, malnutrition, metabolic alterations, and lethargy • Parents often report trying several different baby formulas because they (or their physicians) assume vomiting is due to intolerance
- 4. P/E • Typical clinical features are: projectile vomiting, visible peristalsis, and a palpable pyloric tumor. • Early in the course , the classic signs may be absent. • An enlarged pylorus, classically described as an "olive," can be palpated in the right upper quadrant or epigastrium of the abdomen in 60-80% of infants. • Best felt after vomiting or during, or at the end of, feeding • When diagnosis is delayed, the infant may develop severe constipation associated with signs of dehydration, malnutrition, lethargy, and shock.
- 5. Investigations • U&Es to document adequacy of fluid resuscitation and correction of electrolyte imbalances before surgical repair. The classic biochemical abnormality in hypertrophic pyloric stenosis is hypochloremic, hypokalemic metabolic alkalosis. • Ultrasonography: The criterion standard imaging technique for diagnosing hypertrophic pyloric stenosis • Muscle wall thickness 3 mm or greater and pyloric channel length 14 mm or greater are considered abnormal in infants younger than 30 days • Barium upper GI study: • Endoscopy: Reserved for patients with atypical clinical signs when ultrasonography and UGI studies are nondiagnostic
- 6. Management • Hypertrophic pyloric stenosis is the most common condition requiring surgery in infancy. • Correction of an associated fluid and electrolytes disturbances is vital prior to general anesthesia induction. • Surgical repair of hypertrophic pyloric stenosis is fairly straightforward and without many complications. • However, properly preparing the infant is vitally important.
- 7. Preoperative management • NPO • NGT • IVF :Base fluid resuscitation on the infant's degree of dehydration • Most infants can have their fluid status corrected within 24 hours; however, severely dehydrated children sometimes require several days for correction • Adequate amounts of both chloride and potassium are necessary to correct metabolic alkalosis • Unless renal insufficiency is a concern, initially add 2-4 mEq of KCl per 100 mL of IV fluid • Urine output and serial electrolyte determinations are performed during resuscitation • Correction of serum chloride level to 90 mEq/L or greater is usually adequate to proceed with surgical intervention
- 8. Surgical treatment • Ramstedt pyloromyotomy remains the standard procedure of choice • Laparoscopic pyloromyotomy may also be used • Endoscopic pyloromyotomy is a simple procedure and can be performed as an outpatient procedure • Endoscopic balloon dilatation of hypertrophic pyloric stenosis after failed pyloromyotomy can be used
- 9. Postoperative management • Continue IV maintenance fluid until the infant is able to tolerate enteral feedings • In most instances, feedings can begin within 8 hours following surgery • Addition of an H2 receptor blocker sometimes can be beneficial • Treat persistent vomiting expectantly because it usually resolves within 1-2 days • Avoid the temptation to repeat ultrasonography or upper GI barium study; these invariably demonstrate a deformed pylorus, and results are difficult to interpret